A Rare Case of Double Outlet Right Ventricle with Pulmonary Atresia and Aortopulmonary Window

Abstract

Double outlet right ventricle (DORV), a congenital heart abnormality, occurs when the aorta and pulmonary artery are predominantly or entirely connected to the morphological right ventricle. Classified based on the relationship between the ventricular septal defect (VSD) and the great arteries, DORV exhibits diverse anatomical and hemodynamic variations resembling VSD, tetralogy of Fallot (TOF), transposition of the great arteries (TGA), and functional single ventricle. In this case, we present a coexistence of aortopulmonary window (APW) in a patient with DORV-pulmonary atresia.